Movement Disorders (revue)

Attention, ce site est en cours de développement !
Attention, site généré par des moyens informatiques à partir de corpus bruts.
Les informations ne sont donc pas validées.

Case of symptomatic propriospinal myoclonus evolving toward acute “myoclonic status”

Identifieur interne : 003991 ( Main/Exploration ); précédent : 003990; suivant : 003992

Case of symptomatic propriospinal myoclonus evolving toward acute “myoclonic status”

Auteurs : Mauro Manconi [Italie] ; Barbara Sferrazza [Italie] ; Sandro Iannaccone [Italie] ; Antonio Massimo [Italie] ; Marco Zucconi [Italie] ; Luigi Ferini-Strambi [Italie]

Source :

RBID : ISTEX:CC9AB137DBD1619158AA41B9042B3C2CB11E189D

Descripteurs français

English descriptors

Abstract

Propriospinal myoclonus is a rare motor disorder consisting of involuntary spinal‐generated muscular jerks. Here, we report a severe and uncommon case of propriospinal myoclonus that appeared after a vertebral fracture of T11. In this patient, the polysomnographic investigation showed continuing focal myoclonic activity in axial muscles during stable sleep and an acute progression into a myoclonic “status” associated with respiratory failure and loss of consciousness. It is necessary to consider this severe progression and support it with prompt emergency maneuvers and adequate pharmacotherapy. © 2005 Movement Disorder Society

Url:
DOI: 10.1002/mds.20645


Affiliations:


Links toward previous steps (curation, corpus...)


Le document en format XML

<record>
<TEI wicri:istexFullTextTei="biblStruct">
<teiHeader>
<fileDesc>
<titleStmt>
<title xml:lang="en">Case of symptomatic propriospinal myoclonus evolving toward acute “myoclonic status”</title>
<author>
<name sortKey="Manconi, Mauro" sort="Manconi, Mauro" uniqKey="Manconi M" first="Mauro" last="Manconi">Mauro Manconi</name>
</author>
<author>
<name sortKey="Sferrazza, Barbara" sort="Sferrazza, Barbara" uniqKey="Sferrazza B" first="Barbara" last="Sferrazza">Barbara Sferrazza</name>
</author>
<author>
<name sortKey="Iannaccone, Sandro" sort="Iannaccone, Sandro" uniqKey="Iannaccone S" first="Sandro" last="Iannaccone">Sandro Iannaccone</name>
</author>
<author>
<name sortKey="Massimo, Antonio" sort="Massimo, Antonio" uniqKey="Massimo A" first="Antonio" last="Massimo">Antonio Massimo</name>
</author>
<author>
<name sortKey="Zucconi, Marco" sort="Zucconi, Marco" uniqKey="Zucconi M" first="Marco" last="Zucconi">Marco Zucconi</name>
</author>
<author>
<name sortKey="Ferini Trambi, Luigi" sort="Ferini Trambi, Luigi" uniqKey="Ferini Trambi L" first="Luigi" last="Ferini-Strambi">Luigi Ferini-Strambi</name>
</author>
</titleStmt>
<publicationStmt>
<idno type="wicri:source">ISTEX</idno>
<idno type="RBID">ISTEX:CC9AB137DBD1619158AA41B9042B3C2CB11E189D</idno>
<date when="2005" year="2005">2005</date>
<idno type="doi">10.1002/mds.20645</idno>
<idno type="url">https://api.istex.fr/document/CC9AB137DBD1619158AA41B9042B3C2CB11E189D/fulltext/pdf</idno>
<idno type="wicri:Area/Istex/Corpus">003090</idno>
<idno type="wicri:Area/Istex/Curation">003090</idno>
<idno type="wicri:Area/Istex/Checkpoint">002401</idno>
<idno type="wicri:doubleKey">0885-3185:2005:Manconi M:case:of:symptomatic</idno>
<idno type="wicri:source">PubMed</idno>
<idno type="RBID">pubmed:16092107</idno>
<idno type="wicri:Area/PubMed/Corpus">002F23</idno>
<idno type="wicri:Area/PubMed/Curation">002F23</idno>
<idno type="wicri:Area/PubMed/Checkpoint">003204</idno>
<idno type="wicri:Area/Ncbi/Merge">001389</idno>
<idno type="wicri:Area/Ncbi/Curation">001389</idno>
<idno type="wicri:Area/Ncbi/Checkpoint">001389</idno>
<idno type="wicri:doubleKey">0885-3185:2005:Manconi M:case:of:symptomatic</idno>
<idno type="wicri:Area/Main/Merge">005078</idno>
<idno type="wicri:source">INIST</idno>
<idno type="RBID">Pascal:06-0191539</idno>
<idno type="wicri:Area/PascalFrancis/Corpus">001C20</idno>
<idno type="wicri:Area/PascalFrancis/Curation">001101</idno>
<idno type="wicri:Area/PascalFrancis/Checkpoint">001F10</idno>
<idno type="wicri:doubleKey">0885-3185:2005:Manconi M:case:of:symptomatic</idno>
<idno type="wicri:Area/Main/Merge">005388</idno>
<idno type="wicri:Area/Main/Curation">003991</idno>
<idno type="wicri:Area/Main/Exploration">003991</idno>
</publicationStmt>
<sourceDesc>
<biblStruct>
<analytic>
<title level="a" type="main" xml:lang="en">Case of symptomatic propriospinal myoclonus evolving toward acute “myoclonic status”</title>
<author>
<name sortKey="Manconi, Mauro" sort="Manconi, Mauro" uniqKey="Manconi M" first="Mauro" last="Manconi">Mauro Manconi</name>
<affiliation wicri:level="3">
<country xml:lang="fr">Italie</country>
<wicri:regionArea>Department of Neurology, Vita‐Salute University, Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) San Raffaele‐Turro, Milan</wicri:regionArea>
<placeName>
<settlement type="city">Milan</settlement>
<region nuts="2">Lombardie</region>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Sferrazza, Barbara" sort="Sferrazza, Barbara" uniqKey="Sferrazza B" first="Barbara" last="Sferrazza">Barbara Sferrazza</name>
<affiliation wicri:level="3">
<country xml:lang="fr">Italie</country>
<wicri:regionArea>Department of Neurology, Vita‐Salute University, Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) San Raffaele‐Turro, Milan</wicri:regionArea>
<placeName>
<settlement type="city">Milan</settlement>
<region nuts="2">Lombardie</region>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Iannaccone, Sandro" sort="Iannaccone, Sandro" uniqKey="Iannaccone S" first="Sandro" last="Iannaccone">Sandro Iannaccone</name>
<affiliation wicri:level="3">
<country xml:lang="fr">Italie</country>
<wicri:regionArea>Department of Neurology, Vita‐Salute University, Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) San Raffaele‐Turro, Milan</wicri:regionArea>
<placeName>
<settlement type="city">Milan</settlement>
<region nuts="2">Lombardie</region>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Massimo, Antonio" sort="Massimo, Antonio" uniqKey="Massimo A" first="Antonio" last="Massimo">Antonio Massimo</name>
<affiliation wicri:level="3">
<country xml:lang="fr">Italie</country>
<wicri:regionArea>Department of Neurology, Vita‐Salute University, Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) San Raffaele‐Turro, Milan</wicri:regionArea>
<placeName>
<settlement type="city">Milan</settlement>
<region nuts="2">Lombardie</region>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Zucconi, Marco" sort="Zucconi, Marco" uniqKey="Zucconi M" first="Marco" last="Zucconi">Marco Zucconi</name>
<affiliation wicri:level="3">
<country xml:lang="fr">Italie</country>
<wicri:regionArea>Department of Neurology, Vita‐Salute University, Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) San Raffaele‐Turro, Milan</wicri:regionArea>
<placeName>
<settlement type="city">Milan</settlement>
<region nuts="2">Lombardie</region>
</placeName>
</affiliation>
</author>
<author>
<name sortKey="Ferini Trambi, Luigi" sort="Ferini Trambi, Luigi" uniqKey="Ferini Trambi L" first="Luigi" last="Ferini-Strambi">Luigi Ferini-Strambi</name>
<affiliation wicri:level="3">
<country xml:lang="fr">Italie</country>
<wicri:regionArea>Department of Neurology, Vita‐Salute University, Istituto di Ricovero e Cura a Carattere Scientifico (IRCCS) San Raffaele‐Turro, Milan</wicri:regionArea>
<placeName>
<settlement type="city">Milan</settlement>
<region nuts="2">Lombardie</region>
</placeName>
</affiliation>
</author>
</analytic>
<monogr></monogr>
<series>
<title level="j">Movement Disorders</title>
<title level="j" type="sub">Official Journal of the Movement Disorder Society</title>
<title level="j" type="abbrev">Mov. Disord.</title>
<idno type="ISSN">0885-3185</idno>
<idno type="eISSN">1531-8257</idno>
<imprint>
<publisher>Wiley Subscription Services, Inc., A Wiley Company</publisher>
<pubPlace>Hoboken</pubPlace>
<date type="published" when="2005-12">2005-12</date>
<biblScope unit="vol">20</biblScope>
<biblScope unit="issue">12</biblScope>
<biblScope unit="page" from="1646">1646</biblScope>
<biblScope unit="page" to="1650">1650</biblScope>
</imprint>
<idno type="ISSN">0885-3185</idno>
</series>
<idno type="istex">CC9AB137DBD1619158AA41B9042B3C2CB11E189D</idno>
<idno type="DOI">10.1002/mds.20645</idno>
<idno type="ArticleID">MDS20645</idno>
</biblStruct>
</sourceDesc>
<seriesStmt>
<idno type="ISSN">0885-3185</idno>
</seriesStmt>
</fileDesc>
<profileDesc>
<textClass>
<keywords scheme="KwdEn" xml:lang="en">
<term>Anticonvulsants (therapeutic use)</term>
<term>Clonazepam (therapeutic use)</term>
<term>Disease Progression</term>
<term>Electromyography (methods)</term>
<term>Epilepsies, Myoclonic (drug therapy)</term>
<term>Epilepsies, Myoclonic (etiology)</term>
<term>Epilepsies, Myoclonic (pathology)</term>
<term>Epilepsies, Myoclonic (physiopathology)</term>
<term>Evoked Potentials, Somatosensory (physiology)</term>
<term>Evoked Potentials, Somatosensory (radiation effects)</term>
<term>Eye Movements (physiology)</term>
<term>Female</term>
<term>Humans</term>
<term>Magnetic Resonance Imaging (methods)</term>
<term>Middle Aged</term>
<term>Muscle, Skeletal (drug effects)</term>
<term>Muscle, Skeletal (physiopathology)</term>
<term>Muscle, Skeletal (radiation effects)</term>
<term>Myoclonus</term>
<term>Nervous system diseases</term>
<term>Neural Conduction (radiation effects)</term>
<term>Sleep</term>
<term>Spinal Fractures (complications)</term>
<term>Spinal Fractures (pathology)</term>
<term>Spinal Nerves (drug effects)</term>
<term>Spinal Nerves (pathology)</term>
<term>Spinal Nerves (physiopathology)</term>
<term>Transcranial Magnetic Stimulation (methods)</term>
<term>focal spinal myoclonus</term>
<term>myoclonic status</term>
<term>propriospinal myoclonus</term>
<term>sleep</term>
</keywords>
<keywords scheme="MESH" type="chemical" qualifier="therapeutic use" xml:lang="en">
<term>Anticonvulsants</term>
<term>Clonazepam</term>
</keywords>
<keywords scheme="MESH" qualifier="complications" xml:lang="en">
<term>Spinal Fractures</term>
</keywords>
<keywords scheme="MESH" qualifier="drug effects" xml:lang="en">
<term>Muscle, Skeletal</term>
<term>Spinal Nerves</term>
</keywords>
<keywords scheme="MESH" qualifier="drug therapy" xml:lang="en">
<term>Epilepsies, Myoclonic</term>
</keywords>
<keywords scheme="MESH" qualifier="etiology" xml:lang="en">
<term>Epilepsies, Myoclonic</term>
</keywords>
<keywords scheme="MESH" qualifier="methods" xml:lang="en">
<term>Electromyography</term>
<term>Magnetic Resonance Imaging</term>
<term>Transcranial Magnetic Stimulation</term>
</keywords>
<keywords scheme="MESH" qualifier="pathology" xml:lang="en">
<term>Epilepsies, Myoclonic</term>
<term>Spinal Fractures</term>
<term>Spinal Nerves</term>
</keywords>
<keywords scheme="MESH" qualifier="physiology" xml:lang="en">
<term>Evoked Potentials, Somatosensory</term>
<term>Eye Movements</term>
</keywords>
<keywords scheme="MESH" qualifier="physiopathology" xml:lang="en">
<term>Epilepsies, Myoclonic</term>
<term>Muscle, Skeletal</term>
<term>Spinal Nerves</term>
</keywords>
<keywords scheme="MESH" qualifier="radiation effects" xml:lang="en">
<term>Evoked Potentials, Somatosensory</term>
<term>Muscle, Skeletal</term>
<term>Neural Conduction</term>
</keywords>
<keywords scheme="MESH" xml:lang="en">
<term>Disease Progression</term>
<term>Female</term>
<term>Humans</term>
<term>Middle Aged</term>
</keywords>
<keywords scheme="Pascal" xml:lang="fr">
<term>Myoclonie</term>
<term>Sommeil</term>
<term>Système nerveux pathologie</term>
</keywords>
</textClass>
<langUsage>
<language ident="en">en</language>
</langUsage>
</profileDesc>
</teiHeader>
<front>
<div type="abstract" xml:lang="en">Propriospinal myoclonus is a rare motor disorder consisting of involuntary spinal‐generated muscular jerks. Here, we report a severe and uncommon case of propriospinal myoclonus that appeared after a vertebral fracture of T11. In this patient, the polysomnographic investigation showed continuing focal myoclonic activity in axial muscles during stable sleep and an acute progression into a myoclonic “status” associated with respiratory failure and loss of consciousness. It is necessary to consider this severe progression and support it with prompt emergency maneuvers and adequate pharmacotherapy. © 2005 Movement Disorder Society</div>
</front>
</TEI>
<affiliations>
<list>
<country>
<li>Italie</li>
</country>
<region>
<li>Lombardie</li>
</region>
<settlement>
<li>Milan</li>
</settlement>
</list>
<tree>
<country name="Italie">
<region name="Lombardie">
<name sortKey="Manconi, Mauro" sort="Manconi, Mauro" uniqKey="Manconi M" first="Mauro" last="Manconi">Mauro Manconi</name>
</region>
<name sortKey="Ferini Trambi, Luigi" sort="Ferini Trambi, Luigi" uniqKey="Ferini Trambi L" first="Luigi" last="Ferini-Strambi">Luigi Ferini-Strambi</name>
<name sortKey="Iannaccone, Sandro" sort="Iannaccone, Sandro" uniqKey="Iannaccone S" first="Sandro" last="Iannaccone">Sandro Iannaccone</name>
<name sortKey="Massimo, Antonio" sort="Massimo, Antonio" uniqKey="Massimo A" first="Antonio" last="Massimo">Antonio Massimo</name>
<name sortKey="Sferrazza, Barbara" sort="Sferrazza, Barbara" uniqKey="Sferrazza B" first="Barbara" last="Sferrazza">Barbara Sferrazza</name>
<name sortKey="Zucconi, Marco" sort="Zucconi, Marco" uniqKey="Zucconi M" first="Marco" last="Zucconi">Marco Zucconi</name>
</country>
</tree>
</affiliations>
</record>

Pour manipuler ce document sous Unix (Dilib)

EXPLOR_STEP=$WICRI_ROOT/Wicri/Santé/explor/MovDisordV3/Data/Main/Exploration
HfdSelect -h $EXPLOR_STEP/biblio.hfd -nk 003991 | SxmlIndent | more

Ou

HfdSelect -h $EXPLOR_AREA/Data/Main/Exploration/biblio.hfd -nk 003991 | SxmlIndent | more

Pour mettre un lien sur cette page dans le réseau Wicri

{{Explor lien
   |wiki=    Wicri/Santé
   |area=    MovDisordV3
   |flux=    Main
   |étape=   Exploration
   |type=    RBID
   |clé=     ISTEX:CC9AB137DBD1619158AA41B9042B3C2CB11E189D
   |texte=   Case of symptomatic propriospinal myoclonus evolving toward acute “myoclonic status”
}}

Wicri

This area was generated with Dilib version V0.6.23.
Data generation: Sun Jul 3 12:29:32 2016. Site generation: Wed Feb 14 10:52:30 2024