Case of symptomatic propriospinal myoclonus evolving toward acute “myoclonic status”
Identifieur interne : 003991 ( Main/Exploration ); précédent : 003990; suivant : 003992Case of symptomatic propriospinal myoclonus evolving toward acute “myoclonic status”
Auteurs : Mauro Manconi [Italie] ; Barbara Sferrazza [Italie] ; Sandro Iannaccone [Italie] ; Antonio Massimo [Italie] ; Marco Zucconi [Italie] ; Luigi Ferini-Strambi [Italie]Source :
- Movement Disorders [ 0885-3185 ] ; 2005-12.
Descripteurs français
- Pascal (Inist)
English descriptors
- KwdEn :
- Anticonvulsants (therapeutic use), Clonazepam (therapeutic use), Disease Progression, Electromyography (methods), Epilepsies, Myoclonic (drug therapy), Epilepsies, Myoclonic (etiology), Epilepsies, Myoclonic (pathology), Epilepsies, Myoclonic (physiopathology), Evoked Potentials, Somatosensory (physiology), Evoked Potentials, Somatosensory (radiation effects), Eye Movements (physiology), Female, Humans, Magnetic Resonance Imaging (methods), Middle Aged, Muscle, Skeletal (drug effects), Muscle, Skeletal (physiopathology), Muscle, Skeletal (radiation effects), Myoclonus, Nervous system diseases, Neural Conduction (radiation effects), Sleep, Spinal Fractures (complications), Spinal Fractures (pathology), Spinal Nerves (drug effects), Spinal Nerves (pathology), Spinal Nerves (physiopathology), Transcranial Magnetic Stimulation (methods), focal spinal myoclonus, myoclonic status, propriospinal myoclonus, sleep.
- MESH :
- chemical , therapeutic use : Anticonvulsants, Clonazepam.
- complications : Spinal Fractures.
- drug effects : Muscle, Skeletal, Spinal Nerves.
- drug therapy : Epilepsies, Myoclonic.
- etiology : Epilepsies, Myoclonic.
- methods : Electromyography, Magnetic Resonance Imaging, Transcranial Magnetic Stimulation.
- pathology : Epilepsies, Myoclonic, Spinal Fractures, Spinal Nerves.
- physiology : Evoked Potentials, Somatosensory, Eye Movements.
- physiopathology : Epilepsies, Myoclonic, Muscle, Skeletal, Spinal Nerves.
- radiation effects : Evoked Potentials, Somatosensory, Muscle, Skeletal, Neural Conduction.
- Disease Progression, Female, Humans, Middle Aged.
Abstract
Propriospinal myoclonus is a rare motor disorder consisting of involuntary spinal‐generated muscular jerks. Here, we report a severe and uncommon case of propriospinal myoclonus that appeared after a vertebral fracture of T11. In this patient, the polysomnographic investigation showed continuing focal myoclonic activity in axial muscles during stable sleep and an acute progression into a myoclonic “status” associated with respiratory failure and loss of consciousness. It is necessary to consider this severe progression and support it with prompt emergency maneuvers and adequate pharmacotherapy. © 2005 Movement Disorder Society
Url:
DOI: 10.1002/mds.20645
Affiliations:
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<front><div type="abstract" xml:lang="en">Propriospinal myoclonus is a rare motor disorder consisting of involuntary spinal‐generated muscular jerks. Here, we report a severe and uncommon case of propriospinal myoclonus that appeared after a vertebral fracture of T11. In this patient, the polysomnographic investigation showed continuing focal myoclonic activity in axial muscles during stable sleep and an acute progression into a myoclonic “status” associated with respiratory failure and loss of consciousness. It is necessary to consider this severe progression and support it with prompt emergency maneuvers and adequate pharmacotherapy. © 2005 Movement Disorder Society</div>
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<tree><country name="Italie"><region name="Lombardie"><name sortKey="Manconi, Mauro" sort="Manconi, Mauro" uniqKey="Manconi M" first="Mauro" last="Manconi">Mauro Manconi</name>
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<name sortKey="Ferini Trambi, Luigi" sort="Ferini Trambi, Luigi" uniqKey="Ferini Trambi L" first="Luigi" last="Ferini-Strambi">Luigi Ferini-Strambi</name>
<name sortKey="Iannaccone, Sandro" sort="Iannaccone, Sandro" uniqKey="Iannaccone S" first="Sandro" last="Iannaccone">Sandro Iannaccone</name>
<name sortKey="Massimo, Antonio" sort="Massimo, Antonio" uniqKey="Massimo A" first="Antonio" last="Massimo">Antonio Massimo</name>
<name sortKey="Sferrazza, Barbara" sort="Sferrazza, Barbara" uniqKey="Sferrazza B" first="Barbara" last="Sferrazza">Barbara Sferrazza</name>
<name sortKey="Zucconi, Marco" sort="Zucconi, Marco" uniqKey="Zucconi M" first="Marco" last="Zucconi">Marco Zucconi</name>
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